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Ultrasonography, MRI and classic radiography of skin and MSK involvement in juvenile scleroderma

Marta Idzior
Marta Idzior
, 
Maria Sotniczuk
Maria Sotniczuk
, 
Emil Michalski
Emil Michalski
, 
Piotr Gietka
Piotr Gietka
 oraz 
Iwona Sudoł-Szopińska
Iwona Sudoł-Szopińska
   | 18 gru 2020
Journal of Ultrasonography's Cover Image
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Article Category: research-article
Data publikacji: 18 gru 2020
Zakres stron: 311 - 317
Otrzymano: 30 wrz 2020
Przyjęty: 26 paź 2020
DOI: https://doi.org/10.15557/jou.2020.0054
Słowa kluczowe
© 2021 Polish Ultrasound Society. Published by Medical Communications Sp. z o.o.
This work is licensed under the Creative Commons Attribution-NonCommercial-NoDerivatives 3.0 License.

Fig. 1.

13 y.o. boy with jSS and developmental disorders of the left thigh, left forearm and hand. A. Clinical presentation; B. Gray-scale B-mode with 24 MHz probe shows ill-defined border between the cutis and subcutaneous tissue, their thickening and increased echogenicity, comparing to the contralateral healthy side (left part of the image). C. The affected side shows increased vascularity in SMI comparing to the avascular healthy side. D. Shear wave (SW) elastography on 18 MHz transducer with propagation map taken from the affected area in the subdermal tissue of the thigh and the corresponding contralateral healthy side show an average speed in this area 1.91 m/s with standard deviation (SD) 0.71 m/s. E. SW elastography on the contralateral healthy side was 1.18 m/s and SD 0.18 m/s. F. Strain elastography shows lower tissues elasticity of the affected side. G. Strain elastography on the healthy side, for comparison
13 y.o. boy with jSS and developmental disorders of the left thigh, left forearm and hand. A. Clinical presentation; B. Gray-scale B-mode with 24 MHz probe shows ill-defined border between the cutis and subcutaneous tissue, their thickening and increased echogenicity, comparing to the contralateral healthy side (left part of the image). C. The affected side shows increased vascularity in SMI comparing to the avascular healthy side. D. Shear wave (SW) elastography on 18 MHz transducer with propagation map taken from the affected area in the subdermal tissue of the thigh and the corresponding contralateral healthy side show an average speed in this area 1.91 m/s with standard deviation (SD) 0.71 m/s. E. SW elastography on the contralateral healthy side was 1.18 m/s and SD 0.18 m/s. F. Strain elastography shows lower tissues elasticity of the affected side. G. Strain elastography on the healthy side, for comparison

Fig. 2.

Calcifications in scleroderma. Plain film radiography (AP projection) reveals a collection of calcifications in the soft tissue at the distal phalanx ( A ), ultrasonography confirms calcification in this location ( B ) with twinkling artefact on PD ( C ) Courtesy of Pracoń et al. 14
Calcifications in scleroderma. Plain film radiography (AP projection) reveals a collection of calcifications in the soft tissue at the distal phalanx ( A ), ultrasonography confirms calcification in this location ( B ) with twinkling artefact on PD ( C ) Courtesy of Pracoń et al. 14

Fig. 3.

Calcinosis cutis in a 15-year-old male patient with scleroderma activity, or fibrosis of affected tissues. Such information would be highly appreciated by pediatricians.
Calcinosis cutis in a 15-year-old male patient with scleroderma activity, or fibrosis of affected tissues. Such information would be highly appreciated by pediatricians.

Fig. 4.

Whole body MRI in PD FS sequence, coronal views in a juvenile with scleromyositis: A. increased signal of paravertebral and gluteal muscles, B. increased signal of thigh muscles bilaterally (arrows)
Whole body MRI in PD FS sequence, coronal views in a juvenile with scleromyositis: A. increased signal of paravertebral and gluteal muscles, B. increased signal of thigh muscles bilaterally (arrows)

Classification of juvenile scleroderma(7)

Juvenile systemic scleroderma Juvenile localized scleroderma
Juvenile systemic sclerosis Morphea
Diffuse cutaneous (dcSsc) Plaque morphea
Limited cutaneous (lcSsc) Keloidal morphea
Generalized morphea
Bullous morphea
Skin limited systemic sclerosis Linear scleroderma
(CREST syndrome) Linear morphea
En coup de sabre
Parry-Romberg syndrome - hemifacial atrophy
Overlap syndrome Eosinophilic fasciitis
eISSN:
2451-070X
Język:
Angielski
Częstotliwość wydawania:
4 razy w roku
Dziedziny czasopisma:
Medicine, Basic Medical Science, other
Kanał RSS czasopisma