<abstract xmlns="http://www.w3.org/1999/xhtml"><p> Truncus arteriosus (TA) or common arterial trunk is a rare malformation, accounting for 0.21 to 0.34% of congenital heart diseases, which, if left untreated, leads to increased mortality rates. The condition is characterized by the presence of a unique arterial trunk that overrides the interventricular septum. Despite an overall poor outcome, few subjects present in emergency settings with signs suggestive for pulmonary arterial hypoplasia and associated heart failure. We report the case of a 31-year-old female patient who had been previously diagnosed with pulmonary atresia and severe scoliosis as an infant, presenting in the emergency department with clinical sings of decompensated heart failure which were demonstrated to be attributable to the severe cyanogenic heart malformation and were reversible after initiation of appropriate therapeutic measures.</p></abstract>

Truncus arteriosus (TA) or common arterial trunk is a rare malformation, accounting for 0.21 to 0.34% of congenital heart diseases, which, if left untreated, leads to increased mortality rates. The condition is characterized by the presence of a unique arterial trunk that overrides the interventricular septum. Despite an overall poor outcome, few subjects present in emergency settings with signs suggestive for pulmonary arterial hypoplasia and associated heart failure. We report the case of a 31-year-old female patient who had been previously diagnosed with pulmonary atresia and severe scoliosis as an infant, presenting in the emergency department with clinical sings of decompensated heart failure which were demonstrated to be attributable to the severe cyanogenic heart malformation and were reversible after initiation of appropriate therapeutic measures.

Case Report. Persistent Common Arterial Trunk in an Adult Presenting in the Emergency Room as Severely Decompensated Heart Failure

Journal of Cardiovascular Emergencies

This work is licensed under the Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 License.

Truncus arteriosus (TA) or common arterial trunk is a rare malformation, accounting for 0.21 to 0.34% of congenital heart diseases, which, if left untreated,...

Case Report. Persistent Common Arterial Trunk in an Adult Presenting in the Emergency Room as Severely Decompensated Heart Failure

Pubblicato online: 25 ott 2017

Pagine: 138 - 143

Ricevuto: 11 lug 2017

Accettato: 19 ago 2017

DOI: https://doi.org/10.1515/jce-2017-0018

Parole chiave
common arterial trunk, MAPCA, interventricular septum defect

© 2017

This work is licensed under the Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 License.

Case Report. Persistent Common Arterial Trunk in an Adult Presenting in the Emergency Room as Severely Decompensated Heart Failure

Pubblicato online: 25 ott 2017

Pagine: 138 - 143

Ricevuto: 11 lug 2017

Accettato: 19 ago 2017

DOI: https://doi.org/10.1515/jce-2017-0018

Parole chiavecommon arterial trunk, MAPCA, interventricular septum defect

© 2017

This work is licensed under the Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 License.

Parole chiave
common arterial trunk, MAPCA, interventricular septum defect