<abstract xml:lang="em" xmlns="http://www.w3.org/1999/xhtml"> Background: A new case of congenital pseudarthrosis of the tibia (CPT) presents yearly to CSC, but treatment is prolonged, and not always successful.Objective: To study the outcomes of treatment, and to determine whether a relationship with neurofibromatosis (NF) was of significance.Methods: A review of the medical records at our centre revealed 11 cases of CPT, 5 of which were associated with neurofibromatosis.Results: Most patients had multiple operations for their case of CPT, which did finally lead to union in 6 out of 6 cases with no NF, but in only 1 case out of 5 when NF was present.Conclusion: Late presentation and severe deformity can be overcome, and union can be achieved, but NF has a deleterious effect on obtaining union.</abstract>

Background: A new case of congenital pseudarthrosis of the tibia (CPT) presents yearly to CSC, but treatment is prolonged, and not always successful.Objective: To study the outcomes of treatment, and to determine whether a relationship with neurofibromatosis (NF) was of significance.Methods: A review of the medical records at our centre revealed 11 cases of CPT, 5 of which were associated with neurofibromatosis.Results: Most patients had multiple operations for their case of CPT, which did finally lead to union in 6 out of 6 cases with no NF, but in only 1 case out of 5 when NF was present.Conclusion: Late presentation and severe deformity can be overcome, and union can be achieved, but NF has a deleterious effect on obtaining union.

Delayed presentation of congenital tibial pseudarthrosis and neurofibromatosis: a difficult union

Children’s Surgical Centre, Kien Kleang National Rehabilitation Centre, Phnom Penh,

MB, FACS, FRCSC. Children’s Surgical Centre, Phnom Penh,

Asian Biomedicine

This work is licensed under the Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 License.

Background: A new case of congenital pseudarthrosis of the tibia (CPT) presents yearly to CSC, but treatment is prolonged, and not always successful.Objective:...

Delayed presentation of congenital tibial pseudarthrosis and neurofibromatosis: a difficult union

Article Category: Clinical report

Publié en ligne: 04 févr. 2017

Pages: 111 - 118

DOI: https://doi.org/10.5372/1905-7415.0801.269

Mots clés
Cambodia, congenital pseudarthrosis of tibia, Ilizarov, neurofibromatosis, non-union

© 2017

This work is licensed under the Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 License.

Delayed presentation of congenital tibial pseudarthrosis and neurofibromatosis: a difficult union

Article Category: Clinical report

Publié en ligne: 04 févr. 2017

Pages: 111 - 118

DOI: https://doi.org/10.5372/1905-7415.0801.269

Mots clésCambodia, congenital pseudarthrosis of tibia, Ilizarov, neurofibromatosis, non-union

© 2017

This work is licensed under the Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 License.

Mots clés
Cambodia, congenital pseudarthrosis of tibia, Ilizarov, neurofibromatosis, non-union