<abstract xmlns="http://www.w3.org/1999/xhtml"><p>Left ventricle noncompaction or noncompaction cardiomyopathy is a rare cause of cardiomyopathy, presumed to be the consequence of the cessation of the embryological phenomenon of progressive compaction of the ventricular myocardium (which normally occurs between the 5th and 8th week) with the persistence, to varying degrees, of prominent trabeculae and deep intertrabecular spaces Placed as an unclassified cardiomyopathy, this pathology is of interest due to different contrasting aspects observed in its evolution over time. The article reviews the etiopathogenic hypotheses, the diagnostic criteria according to the imagery used, the clinical forms of presentation and certain general principles of treatment. To illustrate the imagery used in this heart disease, the article has attached images of a case of noncompaction cardiomyopathy in a 26-year-old patient with left ventricular ejection fraction of 17% (measured by cardiac magnetic resonance imaging). Finally, the idea of the need for multicenter studies to establish whether this cardiomyopathy is an independent disease or a distinct phenotype which is not necessarily pathological is supported.</p></abstract>

Left ventricle noncompaction or noncompaction cardiomyopathy is a rare cause of cardiomyopathy, presumed to be the consequence of the cessation of the embryological phenomenon of progressive compaction of the ventricular myocardium (which normally occurs between the 5th and 8th week) with the persistence, to varying degrees, of prominent trabeculae and deep intertrabecular spaces Placed as an unclassified cardiomyopathy, this pathology is of interest due to different contrasting aspects observed in its evolution over time. The article reviews the etiopathogenic hypotheses, the diagnostic criteria according to the imagery used, the clinical forms of presentation and certain general principles of treatment. To illustrate the imagery used in this heart disease, the article has attached images of a case of noncompaction cardiomyopathy in a 26-year-old patient with left ventricular ejection fraction of 17% (measured by cardiac magnetic resonance imaging). Finally, the idea of the need for multicenter studies to establish whether this cardiomyopathy is an independent disease or a distinct phenotype which is not necessarily pathological is supported.

Contrasting Aspects in Noncompaction Cardiomyopathy

“Dr. Carol Davila” Central Emergency University Military Hospital

Internal Medicine

This work is licensed under the Creative Commons Attribution-NonCommercial-NoDerivatives 3.0 License.

{"article-title":"Contrasting Aspects in Noncompaction Cardiomyopathy"}

Left ventricle noncompaction or noncompaction cardiomyopathy is a rare cause of cardiomyopathy, presumed to be the consequence of the cessation of the...

Contrasting Aspects in Noncompaction Cardiomyopathy

Publié en ligne: 05 janv. 2021

Pages: 35 - 44

DOI: https://doi.org/10.2478/inmed-2020-0132

Mots clés
noncompaction cardiomyopathy, ventricular trabeculations, stratified myocardium

© 2020 Lucian-Mihai Ciobîcă et al., published by Sciendo

This work is licensed under the Creative Commons Attribution-NonCommercial-NoDerivatives 3.0 License.

Contrasting Aspects in Noncompaction Cardiomyopathy

Publié en ligne: 05 janv. 2021

Pages: 35 - 44

DOI: https://doi.org/10.2478/inmed-2020-0132

Mots clésnoncompaction cardiomyopathy, ventricular trabeculations, stratified myocardium

© 2020 Lucian-Mihai Ciobîcă et al., published by Sciendo

This work is licensed under the Creative Commons Attribution-NonCommercial-NoDerivatives 3.0 License.

Mots clés
noncompaction cardiomyopathy, ventricular trabeculations, stratified myocardium