<abstract xml:lang="en" xmlns="http://www.w3.org/1999/xhtml"><p>Long QT syndrome (LQTS) is a disorder of myocardial repolarization characterized by prolonged QT interval on ECG with prevalence close to 1/3000-1/5000. LQTS is characterized by the occurrence of syncopal episodes due to torsades de pointes ventricular tachycardia (VT) and by a high risk for sudden cardiac death among untreated patients (1, 2, 3). In 12% of patients with LQTS, sudden death is the first manifestation of the disease and only in 4% this happens in the first year of life (2). There is consensus that all symptomatic children with LQTS should be treated with β-blockers which are effective in preventing cardiac events and reducing mortality in 70%, but do not protect patients from sudden death completely (1,2,3,4). The prognosis is poor in untreated patients with annual mortality 20% and 10 year mortality up to 50% (1, 2). Here we present a case of relatively rare congenital heart rhythm disorders in an infant which required immediate treatment.</p></abstract>

Long QT syndrome (LQTS) is a disorder of myocardial repolarization characterized by prolonged QT interval on ECG with prevalence close to 1/3000-1/5000. LQTS is characterized by the occurrence of syncopal episodes due to torsades de pointes ventricular tachycardia (VT) and by a high risk for sudden cardiac death among untreated patients (1, 2, 3). In 12% of patients with LQTS, sudden death is the first manifestation of the disease and only in 4% this happens in the first year of life (2). There is consensus that all symptomatic children with LQTS should be treated with β-blockers which are effective in preventing cardiac events and reducing mortality in 70%, but do not protect patients from sudden death completely (1,2,3,4). The prognosis is poor in untreated patients with annual mortality 20% and 10 year mortality up to 50% (1, 2). Here we present a case of relatively rare congenital heart rhythm disorders in an infant which required immediate treatment.

Congenital Long QT Syndrome in an Infant

Department for Pediatric Cardiology and Cardiac Surgery, University Hospital for Children, Riga, Latvia

Acta Chirurgica Latviensis

{"article-title":"Congenital Long QT Syndrome in an Infant"}

Long QT syndrome (LQTS) is a disorder of myocardial repolarization characterized by prolonged QT interval on ECG with prevalence close to 1/3000-1/5000. LQTS...

Congenital Long QT Syndrome in an Infant

Publicado en línea: 18 ago 2010

Páginas: 111 - 112

DOI: https://doi.org/10.2478/v10163-010-0023-4

Palabras clave
long QT syndrome, congenital arrhythmia

This content is open access.

Congenital Long QT Syndrome in an Infant

Publicado en línea: 18 ago 2010

Páginas: 111 - 112

DOI: https://doi.org/10.2478/v10163-010-0023-4

Palabras clavelong QT syndrome, congenital arrhythmia

This content is open access.

Palabras clave
long QT syndrome, congenital arrhythmia