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Publicado en línea: 09 oct 2009
Páginas: 61 - 64
DOI: https://doi.org/10.2478/v10034-009-0002-z
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Gorlin's syndrome (GS) is a rare autosomal, dominant syndrome, characterized by multiple basal cell carcinomas, odontogenic keratocysts, a characteristic facial appearance, skeletal anomalies and malignancies of various organs throughout the body. We describe a 14-year-old girl with GS and propose a management protocol.