<abstract xmlns="http://www.w3.org/1999/xhtml"><p>Intraspinal extradural primitive neuroectodermal tumours (PNET) represent a rare entity that almost always carry a poor prognosis. A recent literature research revealed only four cases reported in adults. The tumours have mainly thoracic and lumbar location. We report the only case with cervical location and with the longest survival. Urgent laminectomy was performed resulting in a rapid pain relief for the patient. The patient was followed up with craniospinal irradiation and several cycles of chemotherapy. The patient died due to dissemination of the disease 31 months after the diagnosis. Intraspinal PNET tumours have a rapidly progressive course, and there is no current consensus on the optimal therapeutic approach.</p></abstract>

Intraspinal extradural primitive neuroectodermal tumours (PNET) represent a rare entity that almost always carry a poor prognosis. A recent literature research revealed only four cases reported in adults. The tumours have mainly thoracic and lumbar location. We report the only case with cervical location and with the longest survival. Urgent laminectomy was performed resulting in a rapid pain relief for the patient. The patient was followed up with craniospinal irradiation and several cycles of chemotherapy. The patient died due to dissemination of the disease 31 months after the diagnosis. Intraspinal PNET tumours have a rapidly progressive course, and there is no current consensus on the optimal therapeutic approach.

Cervical intraspinal extradural primitive neuroectodermal tumour in an adult

Department of Radiation Oncology, Aretaieio University Hospital, Athens, 11528 Greece

Department of Medical Oncology, Aretaieio University Hospital, Athens, 11528 Greece

Department of Pathology, Aretaieio University Hospital, Athens, 11528 Greece

Department of Radiology, Aretaieio University Hospital, Athens, 11528 Greece

Forum of Clinical Oncology

This work is licensed under the Creative Commons Attribution-NonCommercial-NoDerivatives 3.0 License.

{"article-title":"Cervical intraspinal extradural primitive neuroectodermal tumour in an adult"}

Intraspinal extradural primitive neuroectodermal tumours (PNET) represent a rare entity that almost always carry a poor prognosis. A recent literature research...

Cervical intraspinal extradural primitive neuroectodermal tumour in an adult

Publicado en línea: 14 ago 2014

Páginas: 1 - 5

DOI: https://doi.org/10.2478/fco-2014-0001

Palabras clave
Extradural, Primitive neuroectodermal, Tumour, Radiotherapy, Chemotherapy

© 2014 Pinelopi V Gogou et. al.

This work is licensed under the Creative Commons Attribution-NonCommercial-NoDerivatives 3.0 License.

Cervical intraspinal extradural primitive neuroectodermal tumour in an adult

Publicado en línea: 14 ago 2014

Páginas: 1 - 5

DOI: https://doi.org/10.2478/fco-2014-0001

Palabras claveExtradural, Primitive neuroectodermal, Tumour, Radiotherapy, Chemotherapy

© 2014 Pinelopi V Gogou et. al.

This work is licensed under the Creative Commons Attribution-NonCommercial-NoDerivatives 3.0 License.

Palabras clave
Extradural, Primitive neuroectodermal, Tumour, Radiotherapy, Chemotherapy