<abstract xmlns="http://www.w3.org/1999/xhtml">

<p>Congenitally corrected transposition of the great arteries (ccTGA) is a rare congenital anomaly defined by double discordance – atrioventricular and ventricular-arterial. ccTGA frequently has associated lesions, which influence long-term survival.</p>
<p>The management of patients with ccTGA regarding the closure of defects and pacing strategies is often very challenging. Moreover, tricuspid valve regurgitation and its impact on the systemic right ventricle requires close monitoring and potentially timely interventions. In this paper, we present and discuss the management challenges raised by a patient with situs inversus totalis, dextrocardia, ccTGA, Ebstein anomaly of the tricuspid valve, atrial septal defect, and complete atrioventricular block.</p>
</abstract>

Congenitally corrected transposition of the great arteries (ccTGA) is a rare congenital anomaly defined by double discordance – atrioventricular and ventricular-arterial. ccTGA frequently has associated lesions, which influence long-term survival.
The management of patients with ccTGA regarding the closure of defects and pacing strategies is often very challenging. Moreover, tricuspid valve regurgitation and its impact on the systemic right ventricle requires close monitoring and potentially timely interventions. In this paper, we present and discuss the management challenges raised by a patient with situs inversus totalis, dextrocardia, ccTGA, Ebstein anomaly of the tricuspid valve, atrial septal defect, and complete atrioventricular block.

Complex Congenital Heart Lesion - Should We Operate or Not?

Romanian Journal of Cardiology

This work is licensed under the Creative Commons Attribution 4.0 International License.

{"article-title":"Complex Congenital Heart Lesion - Should We Operate or Not?"}

Congenitally corrected transposition of the great arteries (ccTGA) is a rare congenital anomaly defined by double discordance – atrioventricular and...

Complex Congenital Heart Lesion - Should We Operate or Not?

Article Category: Case Presentation

Online veröffentlicht: 30. Juni 2024

Seitenbereich: 86 - 91

DOI: https://doi.org/10.2478/rjc-2024-0010

Schlüsselwörter
congenital, transposition, block, situs inversus, dextrocardia, Ebstein-like, septal defect

© 2024 Claudia-Andreea Ene et al., published by Sciendo

This work is licensed under the Creative Commons Attribution 4.0 International License.

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Complex Congenital Heart Lesion - Should We Operate or Not?

Article Category: Case Presentation

Online veröffentlicht: 30. Juni 2024

Seitenbereich: 86 - 91

DOI: https://doi.org/10.2478/rjc-2024-0010

Schlüsselwörtercongenital, transposition, block, situs inversus, dextrocardia, Ebstein-like, septal defect

© 2024 Claudia-Andreea Ene et al., published by Sciendo

This work is licensed under the Creative Commons Attribution 4.0 International License.

Figure 1

Figure 2

Figure 3

Figure 4

Figure 5

Figure 6

Figure 7

Figure 8

Figure 9

Schlüsselwörter
congenital, transposition, block, situs inversus, dextrocardia, Ebstein-like, septal defect