<abstract xmlns="http://www.w3.org/1999/xhtml"><p>Alveolar soft part sarcoma (ASPS) is a rare mesenchymal soft-tissue tumour. It commonly arises in the lower extremities in adults and the head and neck in children. Primary pulmonary involvement, without evidence of soft tissue tumour elsewhere, is very rare. We present the seventh case ever reported in the literature of primary ASPS of the lung, which was revealed by brain metastases in a 28-year-old male patient. The parietal brain tumour was resected. The radiological and histological study led to the diagnosis: metastasis of an alveolar sarcoma. The patient then had brain radiotherapy and chemotherapy. Using this case as a starting point, we reviewed the characteristics and the main therapeutic options in these uncommon neoplasms.</p></abstract>

Alveolar soft part sarcoma (ASPS) is a rare mesenchymal soft-tissue tumour. It commonly arises in the lower extremities in adults and the head and neck in children. Primary pulmonary involvement, without evidence of soft tissue tumour elsewhere, is very rare. We present the seventh case ever reported in the literature of primary ASPS of the lung, which was revealed by brain metastases in a 28-year-old male patient. The parietal brain tumour was resected. The radiological and histological study led to the diagnosis: metastasis of an alveolar sarcoma. The patient then had brain radiotherapy and chemotherapy. Using this case as a starting point, we reviewed the characteristics and the main therapeutic options in these uncommon neoplasms.

Brain metastases revealing primary pulmonary soft part sarcoma

Department of Neurosurgery, Trauma and Burn Center, Ben Arous. Faculty of Medicine of Tunis

Department of Pathology, La Rabta Hospital, Tunis. Faculty of Medicine of Tunis

Pneumologia

This work is licensed under the Creative Commons Attribution-NonCommercial-NoDerivatives 3.0 License.

{"article-title":"Brain metastases revealing primary pulmonary soft part sarcoma"}

Alveolar soft part sarcoma (ASPS) is a rare mesenchymal soft-tissue tumour. It commonly arises in the lower extremities in adults and the head and neck in...

Brain metastases revealing primary pulmonary soft part sarcoma

Online veröffentlicht: 28. Mai 2022

Seitenbereich: 34 - 39

DOI: https://doi.org/10.2478/pneum-2022-0007

Schlüsselwörter
Alveolar soft part sarcoma, brain tumour

© 2021 Kaouther Somrani et al., published by Sciendo

This work is licensed under the Creative Commons Attribution-NonCommercial-NoDerivatives 3.0 License.

Brain metastases revealing primary pulmonary soft part sarcoma

Online veröffentlicht: 28. Mai 2022

Seitenbereich: 34 - 39

DOI: https://doi.org/10.2478/pneum-2022-0007

SchlüsselwörterAlveolar soft part sarcoma, brain tumour

© 2021 Kaouther Somrani et al., published by Sciendo

This work is licensed under the Creative Commons Attribution-NonCommercial-NoDerivatives 3.0 License.

Schlüsselwörter
Alveolar soft part sarcoma, brain tumour