1. bookVolume 4 (2021): Issue 1 (June 2021)
Journal Details
License
Format
Journal
eISSN
2544-8978
First Published
30 May 2018
Publication timeframe
1 time per year
Languages
English
access type Open Access

Malignant granular cell tumor of the arm – case report

Published Online: 13 Aug 2021
Volume & Issue: Volume 4 (2021) - Issue 1 (June 2021)
Page range: 3 - 8
Accepted: 09 Jul 2021
Journal Details
License
Format
Journal
eISSN
2544-8978
First Published
30 May 2018
Publication timeframe
1 time per year
Languages
English
Abstract

Granular cell tumor (GCT) is a rare form of soft tissue cancer that is usually benign. Its malignant evolution is encountered in less than 2% of cases, having a more rapid and unfavorable evolution. Clinical presentation betraying malignant features could be increased tumor size, rapid growth, deep localization, and female gender.

This paper presents the case of a 52-year-old patient with a hard, rapidly evolving tumor in the left arm. The diagnosis of granular cell tumor was made based on histopathological examination using the Fanburg and Smith criteria to differentiate the formation as malignant, but with certainty this was subsequently confirmed by the existence of a metastasis. Surgical excision was performed and the evolution was favorable.

Evolution and treatment differ depending on the benign or malignant form, but surgical treatment with wide local excision is recommended. This may be followed by chemotherapy or radiotherapy, and follow-up of patients for the rest of their lives is mandatory.

Keywords

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