1. bookVolume 2 (2019): Issue 1 (April 2019)
Journal Details
License
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Journal
First Published
30 Sep 2018
Publication timeframe
2 times per year
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English
access type Open Access

Cystic fibrosis related diabetes

Published Online: 04 May 2019
Page range: 23 - 27
Received: 02 Feb 2019
Accepted: 27 Feb 2019
Journal Details
License
Format
Journal
First Published
30 Sep 2018
Publication timeframe
2 times per year
Languages
English
Abstract

Cystic fibrosis related diabetes (CFRD) is a redoubtable complication associated to cystic fibrosis, with an increasing frequency, directly proportional to children life expectancy. Although this complication has similar features with DM type 1 and some with type 2, the evolution and even the response to insulin therapy is different. It is also possible that other factors to influence the CFRD clinical expression and subsequently the disease evolution. Since its 1t diagnosis was associated with more frequent pulmonary exacerbations and with the deterioration of the respiratory status, therefore CFRD must be early and correctly diagnosed and managed. The aim of this paper is to present an overview of the recent updates and recommendations regarding this important CF complication.

Keywords

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